Treatment Experience of Heart Tumors in Children Under 1 Year of Age

Denis Lyazin, L.A. Bockeria, D.O. Berishvili, I.Yu Baryshnikova , I.Ye. Nefedova, O.A. Stepanicheva , E.A. Andreeva

A.N. Bakoulev Scientific Center for Cardiovascular Surgery, Moscow, Russia

Date, time and location: 2018.05.26 08:30, Press Hall, 2F

Abstract

Background:The heart tumor is a rare disease, especially in children. According to various authors the frequency of occurrence in children is 0,28%.

The aim of this presentation is to describe our experience in diagnostics and treatment of children under the 1 year of age with heart neoplasm of different localization.

Methods:Retrospective analysis of 22 patients with heart tumors of various localization was performed. From 2006 to 2016 all these patients were treated in our centre.

Results:The heart tumor was diagnosed prenatally or in the first weeks of life. The following nosologies were found: rhabdomyomas -14, hamartomas -3, fibromas - 4, teratoma -1; myxomas; hemangiomas and lipomas were absent. Two (9,1 %) patients had clinically significant arrhythmias (supraventricular tachycardia and frequent ventricular extrasystole). Surgical treatment underwent 11 children (in age 10 days - 9 months). Indications for surgical intervention was severe clinical condition of the patient due to hemodynamic compromise. Localization of tumors was the following: rhabdomyomas - 4, fibromas of the right ventricle - 2, hamartomas of the right atrium - 2, pericardium teratoma - 1. There was one lethal outcome. A child with multiple rhabdomyomas in conjunction with tuberous sclerosis died after the surgery. Chemotherapy was not performed in any case. In 8 cases surgical removal of the formations was combined by cryodestruction of residual sections of the formations.

Conclusion:Treatment of heart tumors is their surgical removal. Echocardiography is the main method of detecting such neoplasms and helps to determine the indications for surgical intervention. This approach allows avoiding the surgery with extensive injury of the myocardium in neonatal period and in early infancy and ensures the best survival rate and the maximum tumor excision.